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产品基本信息
产品编号:E922020
产品名称:Ethylmalonic Acid
产品CAS:601-75-2
规格含量:10g
产品价格:面议
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产品详细介绍
标准品编号:
E922020
名称:
Ethylmalonic Acid
别名:
Ethyl-propanedioic Acid; 1,1-Propanedicarboxylic Acid; 2-Ethylpropanedioic Acid;Ethylmalonic Acid; NSC 96615; α-Carboxybutyric Acid
CAS号:
601-75-2
分子式:
C₅H₈O₄
外观:
白色固体
熔点:
107-110°C
分子量:
132.11
储存:
-20°C Freezer
溶解度:
DMSO (Slightly), Methanol (Slightly)
种类:
Building Blocks; Miscellaneous;
应用:
Ethylmalonic Acid is used as a diagnostic agent used in the diagnosis of Ethylmalonic encephalopathy which is a rare autosomal recessive inborn error of metabolism.
参考文献
Baertling, F. et al.: Eur. J. Pediat., 173, 1719 (2014); Sudo, Y. et al.: Hu,am Genome Var., 1, 15016 (2014);