Hygroscopic, -20°C Freezer, Under Inert Atmosphere
溶解度:
Water (Slightly)
稳定性:
Hygroscopic
种类:
Standards; Fluorescent Reagents; Carbohydrates and Oligosaccharides;
应用:
A fluorogenic substrate used for the diagnosis of GM2 gangliosidoses in leukocytes. Genetic defects in human b-hexosaminidase isozymes (Hex A & Hex B) result in various clinical and biochemical types of GM2 gangliosidosis. They include Tay Sachs disease, Sandhoff disease and other forms.