产品编号:D454795
产品规格:10mg
产品价格:面议
| 标准品编号: | D454795 |
| 名称: | N-[(3S,4R,5S,6R)-4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate |
| 别名: | [3S-(3α,4β,5β,6β)]-N-[4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate; 2-Acetamido-1,5-imino-1,2,5-trideoxy-D-galactitol 6-Sulfate; DGJNAc 6-Sulfate; 2-acetamido-1,2-dideoxy-d-galacto-nojirimycin 6-Sulfate |
| 参考CAS号: | 117894-14-1 without salt |
| 分子式: | C₈H₁₆N₂O₇S |
| 分子量: | 284.29 |
| 种类: | Building Blocks; |
| 应用: | Deficiency of N-[(3S,4R,5S,6R)-4,5-Dihydroxy-6-(hydroxymethyl)-3-piperidinyl]-acetamide 6-Sulfate sulfatase produces the mucopolysaccharidosis type IV A (MPS IV A, Morquio syndrome type A disease). |
| 参考文献 | |